Surgical Correction of Spine Deformities in Systemic Diseases

Since 1987 thirty two patients with neurofibromatosis Recklinhausen’s disease, 24 patients with Marfan’s syndrome, 11 patients with Ehlers-Danlos syndrome and 14 patients with rare forms of hereditary systemic diseases were operated on for kyphotic-scoliotic deformities. Treatment difficulties were stipulated by the severity deformity, local or general osteoporosis, concomitant pathology of the inner organs and another skeleton segments, as well as high rate of neurologic disorders. High level of correction and firm stability are provided by surgical treatment that includes diskectomy, corporodesis, craniotibial traction, correction and fixation by Harrington-Luque, posterior spondylodesis.