Lamellar congenital ichthyosis in practice of dermatologists
- 作者: Koshkin S.V.1, Chermnykh T.V.1, Evseeva A.L.1, Ryabova V.V.1, Ryabov A.N.2
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隶属关系:
- State Budget Educational Institution of Higher Professional Education of the Health Care Ministry of the Russian Federation “Kirov State Medical Academy”
- Kirov Children’s Clinical Consultative and Diagnostic Centre, the city of Kirov
- 期: 卷 92, 编号 5 (2016)
- 页面: 44-50
- 栏目: CLINICAL CASE REPORTS
- URL: https://bakhtiniada.ru/0042-4609/article/view/116814
- DOI: https://doi.org/10.25208/0042-4609-2016-92-5-44-50
- ID: 116814
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详细
The paper describes 2 cases of congenital lamellar ichthyosis debuting state «collodion baby». Presented features of clinical manifestations: in newborn all skin is covered with a thin dry yellowish-brown film, resembling collodion, also ectropion and eklabium are frequently marked. After some time cracks appear, the film turns into large squamas, which exfoliate completely in 1.5 months, and so the clinical picture of congenital ichthyosis is formed. Timely initiated therapy, including external moisturizers and lipid-replenishing funds, contributed to the rapid relief of clinical symptoms and infectious-inflammatory process.
作者简介
S. Koshkin
State Budget Educational Institution of Higher Professional Education of the Health Care Ministry of the Russian Federation “Kirov State Medical Academy”
编辑信件的主要联系方式.
Email: koshkin_sergei@mail.ru
俄罗斯联邦
T. Chermnykh
State Budget Educational Institution of Higher Professional Education of the Health Care Ministry of the Russian Federation “Kirov State Medical Academy”俄罗斯联邦
A. Evseeva
State Budget Educational Institution of Higher Professional Education of the Health Care Ministry of the Russian Federation “Kirov State Medical Academy”俄罗斯联邦
V. Ryabova
State Budget Educational Institution of Higher Professional Education of the Health Care Ministry of the Russian Federation “Kirov State Medical Academy”俄罗斯联邦
A. Ryabov
Kirov Children’s Clinical Consultative and Diagnostic Centre, the city of Kirov俄罗斯联邦
参考
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